Behcet's syndrome is associated with inflammation of various areas of the body.Symptoms of Behcet's syndrome depend on the body areas affected. Recurrent mouth ulcers are characteristic of Behcet's syndrome. Treatment of Behcet's syndrome depends on the severity and the location of its manifestations. Behcet’s disease, sometimes, Morbus Bechets, or Silk Road disease, is a rare immune-mediated systemic vasculitis. Behcet's syndrome is classically characterized as a triad of symptoms that include recurring crops of mouth ulcers (aphthous ulcers), genital ulcers, and inflammation of a specialized area around the pupil of the eye (the uvea). ] Some sources use the term "Adamantiades’ syndrome" or "Adamandiades- Bechets syndrome", for the work done by Benediktos Adamantiades. The patient must have oral ulcers along with different symptoms as genital ulcers, skin lesions, eye inflammation, pathergy reaction. The pathery test has a specificity of 95% to 100%, but the results are often negative in American and European patients [11]. The etiology is not well-defined, but it is primarily characterized by auto-inflammation of the blood vessels. Although sometimes erroneously referred to as a "diagnosis of exclusion," the diagnosis can sometimes be reached by pathologic examination of the affected areas. Early identification and treatment is essential. Immunosuppressants such as interferon alpha and tumour necrosis factor antagonists may improve though not completely reverse symptoms of ocular Behçet's, which may progress over time despite treatment. When symptoms are limited to the anterior chamber of the eye prognosis is improved. Posterior involvement, particularly optic nerve involvement is a poor prognostic indicator.
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